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Article Details

Case Report

Volume 4, Issue 2 (February Issue)

Aplasia Cutis Congenita Type VI Bart Syndrome: Case Report

Hamda Nassereldine* and Hawraa Zgheib

Pediatric Department, Saida Governmental Hospital, Beirut Arab University, Beirut, Lebanon

*Corresponding author: Hamda Nassereldine, Pediatric Department, Saida Governmental Hospital, Beirut Arab University, Beirut, Lebanon. E-mail: hamda-nasserdine.94@hotmail.com

Received: February 18, 2022; Accepted: March 01, 2022; Published: March 24, 2022

Citation: Nassereldine H, Zgheib H, et al. Aplasia Cutis Congenita Type VI (Bart Syndrome): Case Report. Clin Image Case Rep J. 2022; 4(2): 217.

Aplasia Cutis Congenita Type VI Bart Syndrome: Case Report
Abstract

Bart syndrome is classified as type VI aplasia cutis congenita, presented clinically by absence of skin, nail malformation and epidermolysis bullosa [2]. It is a rare familial disease [1]. The exact incidence is unknown but estimated to be 1-2 in 10000 births [8]. Here we present a case of female newborn born with absent skin diagnosed clinically and managed by skin care, well followed up with complete healing.

Keywords: Absence of skin; Epidermolysis bullosa; Nails dystrophy; Skin care

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